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Why is it called scimitar syndrome?

Published in Cardiovascular Syndrome Names 1 min read

Scimitar syndrome is named for the distinctive curvilinear pattern that appears on a chest radiograph, resembling a scimitar, which is a type of curved sword.

This rare congenital heart condition is characterized by anomalous pulmonary venous return, typically from the right lung, where the pulmonary veins drain into the inferior vena cava instead of the left atrium. This unusual drainage pathway, when viewed on a chest X-ray, creates a unique radiographic density that often takes on the shape of a scimitar.

Understanding the Name

The name "scimitar syndrome" directly reflects the visual diagnostic clue. The malformation of the pulmonary veins, along with associated lung and heart abnormalities, collectively creates an image that strikingly resembles the distinctive curved blade of a scimitar. Therefore, the syndrome's nomenclature serves as a descriptive and memorable reference to its tell-tale radiographic appearance.